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خرید پکیج
تعداد آیتم قابل مشاهده باقیمانده : 3 مورد
نسخه الکترونیک
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Histopathologic features of erythroderma

Histopathologic features of erythroderma
Causes of erythroderma Key histopathologic features
Idiopathic erythroderma Nonspecific features including hyperkeratosis, parakeratosis, acanthosis, and inflammatory infiltrate
Inflammatory dermatoses
Psoriasis Epidermal acanthosis, parakeratosis, Munro microabscesses, dilated tortuous papillary blood vessels
Atopic dermatitis Acanthosis, hyperkeratosis, spongiosis
Dermatitis (other than atopic) Acanthosis, hyperkeratosis, spongiosis
Pityriasis rubra pilaris Acanthosis, hyperkeratosis, alternating ortho- and parakeratosis (horizontal and vertical)
Lichen planus Lymphohistiocytic infiltrate with band-like distribution upper dermis; obscures the dermoepidermal junction
Chronic actinic dermatitis Acanthosis, hyperkeratosis, spongiosis, perivascular chronic inflammatory cell infiltrate, occasional atypical cerebriform lymphoid cells
Papuloerythroderma of Ofuji  
Sarcoidosis Noncaseating epithelial cell-like granulomas in the deep dermis
Drug reactions

Histology varies according to the reaction pattern

  • In exanthematous type, interface dermatitis, vacuolar changes, necrotic keratinocytes, inflammatory infiltrate with eosinophils 
  • In Stevens Johnson syndrome/toxic epidermal necrolysis, partial to full-thickness skin necrosis
Malignancies: hematologic
Cutaneous T cell lymphoma, Sézary syndrome Findings may be subtle and variable. Sézary cells (highly convoluted cerebriform lymphocytes) along the basal layer, lichenoid infiltrate, epidermotropism, Pautrier microabscesses. Absence of spongiosis.
Other lymphomas (Hodgkin's, non-Hodgkin's) Atypical lymphocytes in dermis and epidermis
Leukemias Leukemic cells in dermis and epidermis
Malignancies: solid organ Nonspecific, variable findings
Renal cell carcinoma  
Hepatocellular carcinoma  
Lung  
Colon  
Immunobullous disease
Pemphigus foliaceus, vulgaris Acantholysis
Bullous pemphigoid Subepidermal separation
Paraneoplastic pemphigus Acantholysis, lichenoid infiltrate, necrotic keratinocytes
Connective tissue disease
Dermatomyositis Interface dermatitis
Subacute lupus erythematosus Interface dermatitis
Infections
Scabies Scabies mite at junction of epidermis and stratum corneum; spongiosis, dermal lymphocytic infiltrate
Dermatophytosis Hyphae
Congenital cutaneous candidiasis Hyphae and yeast-like forms
Staphylococcus scalded skin syndrome Vesiculation at level of granular cell layer
Beta-hemolytic streptococcal erythroderma syndrome  
Blood disorders
Hypereosinophilic syndrome Dermal eosinophilic infiltrates
Mastocytosis Dermal mast cell infiltrates
Graft-versus-host disease (GVHD) Interface dermatitis
Erythroderma occurring in the first year of life (congenital/neonatal/infant): additional diagnoses to be considered
Inherited ichthyoses
Epidermolytic hyperkeratosis (bullous congenital ichthyosiform erythroderma) Hyperkeratosis, acanthosis, superficial vacuolation, clumps of irregular eosinophilic granules in the granular layer
Nonbullous congenital ichthyosiform erythroderma Acanthosis, hyperkeratosis, focal parakeratosis
Netherton syndrome Epidermal psoriasiform hyperplasia
Rare ichthyoses Hyperkeratosis
Primary immunodeficiencies Nonspecific features including hyperkeratosis, parakeratosis, acanthosis, and inflammatory infiltrate
Severe combined immunodeficiency (SCID)  
Severe combined immunodeficiency - Omenn syndrome (a form of SCID)  
X-linked ectodermal dysplasia with immunodeficiency  
Ectodermal dysplasias
Ankyloblepharon-ectodermal defects-cleft lip/palate syndrome Nonspecific features including hyperkeratosis, parakeratosis, acanthosis, and inflammatory infiltrate
Miscellaneous
Menkes disease  
Graphic 87724 Version 6.0

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