Pathway intermediate* | Chemically altered forms¶ | Primary routes of excretion | Samples for measurementΔ |
δ-Aminolevulinic acid | None | Kidney | Urine, plasma |
Porphobilinogen | Porphobilin; uroporphyrin | Kidney | Urine, plasma |
Uroporphyrinogen (octacarboxyl porphyrin) I & III | Uroporphyrin I & III | Kidney | Urine, plasma |
Heptacarboxyl porphyrinogen I & III | Heptacarboxyl porphyrin I & III | Kidney | Urine, plasma |
Hexacarboxyl porphyrinogen I & III | Heptacarboxyl porphyrin I & III | Kidney | Urine, plasma |
Pentacarboxyl porphyrinogen I & III | Pentacarboxyl porphyrin I & III | Kidney | Urine, plasma |
Coproporphyrinogen (tetracarboxyl-porphyrinogen) I & III | Coproporphyrin I & III | Kidney and liver | Urine, feces, plasma |
Harderoporphyrinogen (tricarboxyl-porphyrinogen) | Harderoporphyrin | Liver | Feces, erythrocytes |
Protoporphyrinogen IX | Protoporphyrin IX | Liver | Feces, plasma |
Protoporphyrin IX | None | Liver | Feces, erythrocytes |
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