Diagnostic criteria for Behçet syndrome

Criterion	Required features
Recurrent oral ulceration	Aphthous (idiopathic) ulceration, observed by clinician or patient, with at least three episodes in any 12-month period
Plus any two of the following:
Recurrent genital ulceration	Aphthous ulceration or scarring, observed by clinician or patient
Eye lesions	Anterior or posterior uveitis cells in vitreous in slit-lamp examination; or retinal vasculitis documented by ophthalmologist
Skin lesions	Erythema nodosum-like lesions observed by clinician or patient; papulopustular skin lesions or pseudofolliculitis with characteristic acneiform nodules observed by clinician
Pathergy test	Interpreted at 24 to 48 hours by clinician

Adapted from International Study Group for Behcet's Disease. Criteria for diagnosis of Behcet's disease. Lancet 1990; 335:1078.

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