Location | Other related tumor conditions | First-choice radiopharmaceutical | Second-choice radiopharmaceutical | |
SDHB | Adrenal/extra-adrenal | GISTs, RCCs, and pituitary adenomas | 68Ga-DOTA-SSAs | 18F-FDG |
SDHD | Adrenal/extra-adrenal | GISTs, RCCs, and pituitary adenomas | 68Ga-DOTA-SSAs | 18F-FDG |
SDHC | Adrenal/extra-adrenal | GISTs and RCCs | 68Ga-DOTA-SSAs | 18F-FDG |
FH | Adrenal/extra-adrenal | Skin and uterine leiomyomas, RCCs, uterine leiomyosarcomas, and ovarian mucinous cystadenomas | 18F-FDOPA | 68Ga-DOTA-SSAs |
VHL | Adrenal/extra-adrenal | RCCs, CNS hemangioblastomas, and pancreatic and testicular tumors | 18F-FDOPA | 68Ga-DOTA-SSAs |
EPAS1/HIF2A | Adrenal/extra-adrenal | Somatostatinomas | 18F-FDOPA | 18F-FDG |
MEN2 | Adrenal | MTC, parathyroid adenomas, or hyperplasia | 18F-FDOPA | 68Ga-DOTA-SSAs |
NF1 | Adrenal | Neurofibromas, peripheral nerve sheath tumors, and gliomas | 18F-FDOPA | 68Ga-DOTA-SSAs |
TMEM127 | Adrenal | RCCs | 18F-FDOPA | 68Ga-DOTA-SSAs |
MAX | Adrenal/extra-adrenal | Renal oncocytomas | 18F-FDOPA | 68Ga-DOTA-SSAs |
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