Cardiovascular screening and monitoring for girls and women with Turner syndrome

Screening: All patients at time of diagnosis

Evaluation by cardiologist with expertise in congenital heart disease

Comprehensive examination including blood pressure in both upper and lower extremities

All require clear imaging of heart, aortic valve, aortic arch, and pulmonary veins:

Echocardiography is usually adequate for infants and young girls
CMR imaging and echocardiography for older girls and adults

ECG

Monitoring: Follow-up depends on clinical situation

For patients with apparently normal cardiovascular system and age-appropriate blood pressure:

Reevaluation with imaging at timely occasions (eg, at transition to adult clinic) before attempting pregnancy or with appearance of hypertension; girls who have only had echocardiography should undergo CMR when old enough to cooperate with the procedure
Otherwise, imaging with echocardiography or CMR approximately every 5 years in children and every 10 years in adults

For patients with cardiovascular pathology, treatment and monitoring determined by cardiologist

CMR: cardiovascular magnetic resonance; ECG: electrocardiogram.

Republished with permission of The Endocrine Society, from: Bondy CA, Turner Syndrome Study Group. Care of girls and women with Turner syndrome: a guideline of the Turner Syndrome Study Group. J Clin Endocrinol Metab 2007; 92:10; permission conveyed through Copyright Clearance Center, Inc.

Graphic 106468 Version 6.0

خرید پکیج

Cardiovascular screening and monitoring for girls and women with Turner syndrome